RT Journal Article
SR Electronic
T1 Erdheim-Chester Disease Mimicking Multiple Meningiomas Syndrome
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 134
OP 137
VO 25
IS 1
A1 Johnson, Mahlon D.
A1 Aulino, Joseph P.
A1 Jagasia, Madan
A1 Mawn, Louise A.
YR 2004
UL http://www.ajnr.org/content/25/1/134.abstract
AB Summary: We describe a rare case of non-Langerhans histiocytosis, consistent with Erdheim-Chester disease (ECD), which presented with lesions resembling multiple meningiomas. The patient was initially evaluated for migraine headaches. Initial MR imaging demonstrated a parasellar mass and a second mass near the torcula considered to represent meningiomas. Within 1 year, he developed bilateral orbital lesions surrounding both optic nerves, which were also considered meningiomas. Biopsy of one orbital mass revealed a non-Langerhans histiocytosis. Subsequently, soft tissue masses, a pericardial effusion, and bone lesions consistent with ECD were identified.