RT Journal Article
SR Electronic
T1 Spinal Arteriovenous Malformations Associated with Klippel-Trenaunay-Weber Syndrome: A Literature Search and Report of Two Cases
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 584
OP 589
VO 28
IS 3
A1 Rohany, M.
A1 Shaibani, A.
A1 Arafat, O.
A1 Walker, M.T.
A1 Russell, E.J.
A1 Batjer, H.H.
A1 Getch, C.C.
YR 2007
UL http://www.ajnr.org/content/28/3/584.abstract
AB SUMMARY: Patients with Klippel-Trenaunay-Weber syndrome present with venous varices, cutaneous capillary malformations, and tissue hypertrophy, usually involving an extremity. A small but important subset also harbors arteriovenous malformations (AVMs) of the spine. We report 2 such cases, 1 with 3 concurrent spinal arteriovenous fistulas. These cases and our review of the literature emphasize the importance of screening the spine for AVMs. In addition, it is also important to investigate for the presence of multiple spinal AVMs.